Overview BSEP Function Rescue During Childhood Inhereditary Cholestatic Diseases Status: Not yet recruiting Trial end date: 2023-12-30 Target enrollment: Participant gender: Summary The purpose of the study is to improve the prognosis of inhereditary cholestasis caused by ABCB11 gene mutations by using BSEP function rescue drugs Phase: Phase 2/Phase 3 Details Lead Sponsor: Children's Hospital of Fudan UniversityTreatments: 4-phenylbutyric acid